ETFDH Antibody (PACO26561)
- SKU:
- PACO26561
- Product type:
- Antibody
- Reactivity:
- Pig
- Host Species:
- Rabbit
- Isotype:
- IgG
- Application:
- ELISA
- Antibody type:
- Polyclonal
- Conjugation:
- Unconjugated
Frequently bought together:
Description
抗体名: | ETFDH Antibody (PACO26561) |
抗体コード: | PACO26561 |
サイズ: | 50ug |
宿主種: | Rabbit |
申し込み: | ELISA |
推奨される希釈: | |
反応性: | Pig |
免疫原: | Recombinant Pig Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial protein (34-617AA) |
憲法: | Liquid |
ストレージバッファ: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, PH 7.4 |
精製方法: | >95%, Protein G purified |
抗体のクローン性: | Polyclonal |
アイソタイプ: | IgG |
Conjugate: | Non-conjugated |
バックグラウンド: | Accepts electrons from ETF and reduces ubiquinone. |
シノニム: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial (ETF-QO) (ETF-ubiquinone oxidoreductase) (EC 1.5.5.1) (Electron-transferring-flavoprotein dehydrogenase) (ETF dehydrogenase), ETFDH |
UniProt Protein Function: | ETFDH: Accepts electrons from ETF and reduces ubiquinone. Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C). GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Belongs to the ETF-QO/FixC family.Protein type: EC 1.5.5.1; Membrane protein, integral; Mitochondrial; Oxidoreductase |
UniProt Protein Details: | |
NCBI Summary: | |
UniProt Code: | P55931 |
NCBI GenInfo Identifier: | 298286807 |
NCBI Gene ID: | 100515785 |
NCBI Accession: | P55931.2 |
UniProt Secondary Accession: | P55931 |
UniProt Related Accession: | P55931, AAB30031 |
Molecular Weight: | 80.8kD |
NCBI Full Name: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
NCBI Synonym Full Names: | |
NCBI Official Symbol: | ETFDH |
NCBI Official Synonym Symbols: | ETF-QO |
NCBI Protein Information: | electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
UniProt Protein Name: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
UniProt Synonym Protein Names: | Electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase |
Protein Family: | Electron transfer flavoprotein-ubiquinone oxidoreductase |
UniProt Gene Name: | ETFDH |
UniProt Entry Name: |