ATP7A Antibody, FITC conjugated (PACO55400)
- SKU:
- PACO55400
- Product type:
- Antibody
- Reactivity:
- Human
- Host Species:
- Rabbit
- Isotype:
- IgG
- Application:
- ELISA
- Antibody type:
- Polyclonal
- Conjugation:
- FITC
Frequently bought together:
Description
抗体名: | ATP7A Antibody, FITC conjugated (PACO55400) |
抗体コード: | PACO55400 |
サイズ: | 50ug |
宿主種: | Rabbit |
申し込み: | ELISA |
推奨される希釈: | |
反応性: | Human |
免疫原: | Recombinant Human Copper-transporting ATPase 1 protein (257-488AA) |
憲法: | Liquid |
ストレージバッファ: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, pH 7.4 |
精製方法: | >95%, Protein G purified |
抗体のクローン性: | Polyclonal |
アイソタイプ: | IgG |
Conjugate: | FITC |
バックグラウンド: | May supply copper to copper-requiring proteins within the secretory pathway, when localized in the trans-Golgi network. Under conditions of elevated extracellular copper, it relocalized to the plasma membrane where it functions in the efflux of copper from cells. |
シノニム: | Copper-transporting ATPase 1 (EC 3.6.3.54) (Copper pump 1) (Menkes disease-associated protein), ATP7A, MC1 MNK |
UniProt Protein Function: | May supply copper to copper-requiring proteins within the secretory pathway, when localized in the trans-Golgi network. Under conditions of elevated extracellular copper, it relocalized to the plasma membrane where it functions in the efflux of copper from cells. |
NCBI Summary: | This gene encodes a transmembrane protein that functions in copper transport across membranes. This protein is localized to the trans Golgi network, where it is predicted to supply copper to copper-dependent enzymes in the secretory pathway. It relocalizes to the plasma membrane under conditions of elevated extracellular copper, and functions in the efflux of copper from cells. Mutations in this gene are associated with Menkes disease, X-linked distal spinal muscular atrophy, and occipital horn syndrome. Alternatively-spliced transcript variants have been observed. [provided by RefSeq, Aug 2013] |
UniProt Code: | Q04656 |
NCBI GenInfo Identifier: | 223590241 |
NCBI Gene ID: | 538 |
NCBI Accession: | Q04656.3 |
UniProt Secondary Accession: | Q04656,O00227, O00745, Q9BYY8, B1AT72, |
UniProt Related Accession: | Q04656 |
Molecular Weight: | 11,522 Da |
NCBI Full Name: | Copper-transporting ATPase 1 |
NCBI Synonym Full Names: | ATPase copper transporting alpha |
NCBI Official Symbol: | ATP7A |
NCBI Official Synonym Symbols: | MK; MNK; DSMAX; SMAX3 |
NCBI Protein Information: | copper-transporting ATPase 1 |
UniProt Protein Name: | Copper-transporting ATPase 1 |
UniProt Synonym Protein Names: | Copper pump 1; Menkes disease-associated protein |
UniProt Gene Name: | ATP7A |
UniProt Entry Name: | ATP7A_HUMAN |