BBOX1 Antibody, HRP conjugated (PACO53439)
- SKU:
- PACO53439
- Product type:
- Antibody
- Reactivity:
- Human
- Host Species:
- Rabbit
- Isotype:
- IgG
- Application:
- ELISA
- Antibody type:
- Polyclonal
- Conjugation:
- HRP
Frequently bought together:
Description
抗体名: | BBOX1 Antibody, HRP conjugated (PACO53439) |
抗体コード: | PACO53439 |
サイズ: | 50ug |
宿主種: | Rabbit |
申し込み: | ELISA |
推奨される希釈: | |
反応性: | Human |
免疫原: | Recombinant Human Gamma-butyrobetaine dioxygenase protein (154-247AA) |
憲法: | Liquid |
ストレージバッファ: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, pH 7.4 |
精製方法: | >95%, Protein G purified |
抗体のクローン性: | Polyclonal |
アイソタイプ: | IgG |
Conjugate: | HRP |
バックグラウンド: | Catalyzes the formation of L-carnitine from gamma-butyrobetaine. |
シノニム: | Gamma-butyrobetaine dioxygenase (EC 1.14.11.1) (Gamma-butyrobetaine hydroxylase) (Gamma-BBH) (Gamma-butyrobetaine,2-oxoglutarate dioxygenase), BBOX1, BBH BBOX |
UniProt Protein Function: | BBOX1: Catalyzes the formation of L-carnitine from gamma- butyrobetaine. Belongs to the gamma-BBH/TMLD family. |
UniProt Protein Details: | Protein type:EC 1.14.11.1; Oxidoreductase; Amino Acid Metabolism - lysine degradation Chromosomal Location of Human Ortholog: 11p14.2 Cellular Component: mitochondrion; cytosol Molecular Function:gamma-butyrobetaine dioxygenase activity; zinc ion binding; iron ion binding Biological Process: carnitine biosynthetic process |
NCBI Summary: | This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008] |
UniProt Code: | O75936 |
NCBI GenInfo Identifier: | 5915798 |
NCBI Gene ID: | 8424 |
NCBI Accession: | O75936.1 |
UniProt Secondary Accession: | O75936,Q6IBJ2, B2R8L7, D3DQZ1, |
UniProt Related Accession: | O75936 |
Molecular Weight: | 387 |
NCBI Full Name: | Gamma-butyrobetaine dioxygenase |
NCBI Synonym Full Names: | butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1 |
NCBI Official Symbol: | BBOX1 |
NCBI Official Synonym Symbols: | BBH; BBOX; G-BBH; gamma-BBH |
NCBI Protein Information: | gamma-butyrobetaine dioxygenase; gamma-butyrobetaine hydroxylase; gamma-butyrobetaine,2-oxoglutarate dioxygenase 1 |
UniProt Protein Name: | Gamma-butyrobetaine dioxygenase |
UniProt Synonym Protein Names: | Gamma-butyrobetaine hydroxylase; Gamma-BBH; Gamma-butyrobetaine,2-oxoglutarate dioxygenase |
Protein Family: | Gamma-butyrobetaine dioxygenase |
UniProt Gene Name: | BBOX1 |
UniProt Entry Name: | BODG_HUMAN |